I looked through the medical literature for an association as I personally have not seen hearing loss in patients with HNPP, and there were no cases reported - which doesn't necessarily mean there isn't a connection. However, hearing loss in Friedrich's ataxia is well known. From the description of your symptoms and family history, I suspect you do have some kind of hereditary neuropathy. A formal neurology examination as well as EMG testing are definitely warranted for you and possibly your son. If it is Friedrich's ataxia, then this could have tremendous health implications down the line regarding your heart. There are a multitude of other hereditary neuropathies that can cause these symptoms too like Charcot Marie Tooth disease. Fortunately, there is genetic testing (simple blood test) available for many of these diseases including HNPP and Friedrich's ataxia. Talk to your doctor about getting a referral. The top neuromuscular specialists at the Cleveland Clinic are Bob Shields and Kerry Levin, both of whom are kind and compassionate physicians and are well respected in their field. Best of luck.