Dear Hanna:
Landau Kluffner syndrome should have an EEG finding, especially during sleep. If the EEG did not show sleep, then this is problematic and should be repeated to include sleep if this is expected. Breath-holding and subsequent seizures due to the breath holding spell should have no impact on language. If the seizure event occurred after the breath holding spell, it was likely due to the breath holding spell itself. If a seizure event occurred at another time, this would be a different story and would need to be pursued.A BAEP test lets one know about the integrity of the nerve connections in hearing. It can be a problematic or difficult test in youngsters as normative values are sometimes lacking in a particular lab doing the examination. Your pediatric neurologist should be aware of this and therefore not a problem.
CCF Neuro MD
katie is also going to have a ABR done due to her of verbal auditory agnosia,, i was woundering what kinds o fthings can be rulled out or idebtified by a ABR test could it give us a good idea of what her hearing is like or why she is having problems in localization in her right ear oh also she has a siezure disorder can breath holdind siezures cause problems with language developement she has had 3 normal eegs but her nuerologist lastime was talking about LKS due to a stop of language development and the agnosia which developed after her first sieze could this be possible with a normal eeg?
Dear Hanna:
Sorry that you have to ask all these questions, your surgeon should be the one answering these for you. The lipoma in the spinal cord is an indication that secondary neuralation was abnormal. This is confirmed in the congenital abnormality seen in your daughter. In 100% of disorders of this type the filum and conus of the spinal tract are abnormal. The lipoma should not return once it is removed. Scoliosis will be a life long problems with the need to carefully watch your daughters scolosis as she grows. Surgery to keep the back straight may have to be performed, but only the neurosurgeon can tell you when, and under what circumstances as only he/she knows the compromise of the scoliosis is having on your daughter. The pediatric urologist can better tell you what dynamic studies are best in your daughter as he/she has seen the films and done the initial examination of your daughter. Many children with this type of disorder have bladder problems. I would imagine a VCUG would be the initial test. The surgical techiniques involved depend on the extent of the lipoma and congenital abnormality, and the neurosurgeon knows this best and can tell you the procedure he/she recommends.
I am sorry I can't help you more.
Sincerely,
CCF Neuro MD